Esferocitosis hereditaria. Carolina Cózar Trastorno hemolítico familiar caracterizado por: anemia ictericia intermitente esplenomegalia. Esferocitosis Hereditaria Anemia Esferocitosis Hereditaria 1) Defecto de la membrana del eritrocito. 2) Retención selectiva por el bazo normal. De esta forma es posible el rastreo de la esferocitosis hereditaria y de la Las manifestaciones clínicas como ictericia, esplenomegalia, anemia, aplasia y y sobrecarga de hierro sugiere daño pancréatico por la acumulación, tal como se.

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Thrombo-embolic disease after splenectomy for hereditary stomatocytosis. Am J Hematol ;57 1: Se recomienda el monitoreo de glucemia y ferritina. Long-term evaluation of the beneficial effect of subtotal splenectomy for management of hereditary spherocytosis.

Monitoring of blood glucose and ferritin is recommended. Hereditary spherocytosis, thrombocytosis, and chronic pulmonary emboli: Erythroid membrane protein defects in hereditary spherocytosis. Int J Pediatr Hematol Oncol ; 2: Splenectomy for hereditary spherocytosis: The high association of HS with both diabetes and iron overload suggest damage of the endocrine pancreas by the latter, as it is also seen in genetic hemochromatosis.


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Hereditary Spherocytosis in Neonates with Hyperbilirubinemia. Guidelines for the diagnosis and management of hereditary spherocytosis update. Applying criteria such as permanence of an esferocotosis percentage of spherocytes, family history, biochemical symptoms of hemolysis and clinical data, we claim a prevalence of generally asymptomatic hereditary spherocytosis HS of 1: Clinico-hematological profile of hereditary spherocytosis: A study of 62 Spanish cases. Polish Academjy of Sciences?

Journal of Medical Cases.

Esferocitosis hereditaria by Jazmin Cózar Madero on Prezi

Abstract Hematological automates using double beam laser diffraction by artificially spherized red blood cells determine both volume and hemoglobin concentration of a very large number of cells, even indicating percentages of aberrant elements. Postoperative pulmonary embolism in a young female accompanying with Factor V Leiden mutation and hereditary sypherocytosis.

This explains the discrepancy between these values. HS being a hemolytic defect, frequently increased iron overload was not unexpected.

Anemia Esferocitosis Hereditaria by Danna flores cuadros on Prezi

The Italian survey on hereditary spherocytosis. Servicio de ayuda de la revista. Oxygen affinity and compensated hemolysis in hereditary spherocytosis.

Revista Cubana Hematol Inmunol Hemoter ;18 1: The identity of hyperchromic RBC and spherocytes as well as their normal percentage have been previously established.


Bienvenido a siicsalud Contacto Inquietudes.

Patient and physician should be informed of the presence of HS to avoid misinterpretation of concurrent pathological symptoms. Laparoscopic partial vs total splenectomy in children with hereditary spherocytosis. Blood Cells Mol Dis ; King on behalf of the General Haematology Task Force of the British Committee for Standards in Haematology Guidelines for the diagnosis and management of hereditary spherocytosis.

Clinical symptoms such as jaundice, splenomegaly, anemia, aplasia and biliary calculi prompting a diagnosis of HS are in reality rare. J Thromb Thrombolysis ;17 3: De esta forma es posible el rastreo de la esferocitosis hereditaria y de la esferocitosis esferoctosis. Aires, Argentina; 16 2: J Lab Clin Med.

Este hecho explica la discrepancia entre estos valores. Br J Haematol ;93 2: Thus it becomes possible to screen for both ;or and secondary spherocytosis.

Referencias -Mayelin Herrera Garcia.